Behçet's Disease is one of the systemic vasculitis which has an unknown etiology. Secondary Amiloidosis is a rare complication of Behçet's syndrome. In this article, we discussed a patient, who was accepted in the hospital as a nephrotic syndrome after detailed investigations diagnosed as a Behçet's syndrome. In that patient, we determined secondary amiloidosis by kidney biopsy. Being a very rare association, we also looked over the literature.
Behçet sendromu, etiyolojisi bilinmeyen, sistemik vaskülitle seyreden bir hastalıktır. Sekonder amiloidozis, nadir rastlanan bir bulgusudur. Burada, nefrotik sendrom ile başvuran, Behçet tanısı almış hastamızda böbrek biyopsisi ile sekonder amiloidozis saptanmış ve nadir rastlanan bir olgu olması nedeniyle literatür gözden geçirilmiştir.